{"id":501,"date":"2021-12-17T11:39:51","date_gmt":"2021-12-17T14:39:51","guid":{"rendered":"https:\/\/reumatologiarosario.com.ar\/web\/?page_id=501"},"modified":"2022-02-23T14:58:45","modified_gmt":"2022-02-23T17:58:45","slug":"lupus-eritematoso-sistemico","status":"publish","type":"page","link":"https:\/\/reumatologiarosario.com.ar\/web\/lupus-eritematoso-sistemico\/","title":{"rendered":"Lupus Eritematoso Sist\u00e9mico"},"content":{"rendered":"<p>[et_pb_section fb_built=\u00bb1&#8243; admin_label=\u00bbHero\u00bb _builder_version=\u00bb3.22&#8243; custom_padding=\u00bb0|0px|54px|0px|false|false\u00bb bottom_divider_height=\u00bb0px\u00bb border_width_bottom=\u00bb1px\u00bb border_color_bottom=\u00bb#efefef\u00bb global_colors_info=\u00bb{}\u00bb][et_pb_row column_structure=\u00bb1_2,1_2&#8243; _builder_version=\u00bb3.25&#8243; width=\u00bb100%\u00bb max_width=\u00bb100%\u00bb custom_margin=\u00bb|||\u00bb custom_margin_tablet=\u00bb||0px|\u00bb custom_margin_phone=\u00bb\u00bb custom_margin_last_edited=\u00bbon|desktop\u00bb custom_padding=\u00bb0|0px|7px|0px|false|false\u00bb use_custom_width=\u00bbon\u00bb width_unit=\u00bboff\u00bb custom_width_percent=\u00bb100%\u00bb global_colors_info=\u00bb{}\u00bb][et_pb_column type=\u00bb1_2&#8243; _builder_version=\u00bb3.25&#8243; custom_padding=\u00bb6%||6%|12%\u00bb custom_padding_tablet=\u00bb50px|50px|50px|50px\u00bb custom_padding_phone=\u00bb50px|50px|50px|50px\u00bb custom_padding_last_edited=\u00bbon|tablet\u00bb global_colors_info=\u00bb{}\u00bb padding_tablet=\u00bb50px|50px|50px|50px\u00bb padding_last_edited=\u00bbon|tablet\u00bb custom_padding__hover=\u00bb|||\u00bb padding_phone=\u00bb50px|50px|50px|50px\u00bb][et_pb_image src=\u00bbhttp:\/\/reumatologiarosario.com.ar\/web\/wp-content\/uploads\/2021\/10\/health-icon-10-3.png\u00bb title_text=\u00bbhealth-icon-10-3&#8243; align_tablet=\u00bbcenter\u00bb align_phone=\u00bbcenter\u00bb align_last_edited=\u00bbon|desktop\u00bb _builder_version=\u00bb4.14.1&#8243; global_colors_info=\u00bb{}\u00bb][\/et_pb_image][et_pb_text _builder_version=\u00bb4.14.1&#8243; text_font=\u00bbMontserrat|300|||||||\u00bb text_text_color=\u00bb#677a92&#8243; text_font_size=\u00bb16px\u00bb text_line_height=\u00bb1.8em\u00bb header_font=\u00bbMontserrat||||||||\u00bb header_font_size=\u00bb50px\u00bb header_line_height=\u00bb1.3em\u00bb header_2_font=\u00bb||||||||\u00bb max_width=\u00bb600px\u00bb custom_margin=\u00bb|||\u00bb custom_margin_tablet=\u00bb0px|50px||50px\u00bb custom_margin_phone=\u00bb|20px||\u00bb custom_margin_last_edited=\u00bboff|desktop\u00bb custom_padding=\u00bb|||\u00bb text_line_height_tablet=\u00bb1.8em\u00bb text_line_height_phone=\u00bb1.8em\u00bb text_line_height_last_edited=\u00bbon|phone\u00bb header_font_size_tablet=\u00bb\u00bb header_font_size_phone=\u00bb36px\u00bb header_font_size_last_edited=\u00bbon|phone\u00bb header_2_font_size_phone=\u00bb30px\u00bb header_2_font_size_last_edited=\u00bboff|desktop\u00bb locked=\u00bboff\u00bb global_colors_info=\u00bb{}\u00bb]<\/p>\n<h1>Lupus Eritematoso Sist\u00e9mico<\/h1>\n<p>&nbsp;<\/p>\n<p>[\/et_pb_text][et_pb_text _builder_version=\u00bb4.14.7&#8243; text_font=\u00bbMontserrat|300|||||||\u00bb text_font_size=\u00bb16px\u00bb text_line_height=\u00bb2em\u00bb link_font=\u00bb||||||||\u00bb ul_font=\u00bb||||||||\u00bb ol_font=\u00bb||||||||\u00bb quote_font=\u00bb||||||||\u00bb header_font=\u00bb||||||||\u00bb header_2_font=\u00bbMontserrat|300|||||||\u00bb header_2_text_color=\u00bb#212d3b\u00bb header_2_font_size=\u00bb40px\u00bb header_2_line_height=\u00bb1.5em\u00bb max_width=\u00bb600px\u00bb custom_margin=\u00bb|||\u00bb custom_margin_tablet=\u00bb0px|50px||50px\u00bb custom_margin_last_edited=\u00bboff|desktop\u00bb custom_padding=\u00bb|||\u00bb locked=\u00bboff\u00bb global_colors_info=\u00bb{}\u00bb]<\/p>\n<p style=\"text-align: justify;\"><span>El\u00a0<\/span><strong>lupus eritematoso sist\u00e9mico (LES)<\/strong><span>\u00a0es una\u00a0<\/span>enfermedad autoinmune cr\u00f3nica multisist\u00e9mica<span>\u00a0cuyas manifestaciones son muy variables.\u00a0<\/span><\/p>\n<p>[\/et_pb_text][\/et_pb_column][et_pb_column type=\u00bb1_2&#8243; _builder_version=\u00bb3.25&#8243; custom_padding=\u00bb|||\u00bb global_colors_info=\u00bb{}\u00bb custom_padding__hover=\u00bb|||\u00bb][et_pb_image src=\u00bbhttp:\/\/reumatologiarosario.com.ar\/web\/wp-content\/uploads\/2021\/10\/doctor-02.jpg\u00bb title_text=\u00bbdoctor-02&#8243; force_fullwidth=\u00bbon\u00bb align_tablet=\u00bbcenter\u00bb align_phone=\u00bbcenter\u00bb align_last_edited=\u00bbon|desktop\u00bb _builder_version=\u00bb4.14.1&#8243; custom_margin=\u00bb|||\u00bb custom_padding=\u00bb|||\u00bb animation_style=\u00bbslide\u00bb animation_direction=\u00bbright\u00bb animation_intensity_slide=\u00bb5%\u00bb border_radii=\u00bb||||30vw\u00bb border_color_all=\u00bb#0ee1f4&#8243; border_width_left=\u00bb2vw\u00bb border_color_left=\u00bb#37dfff\u00bb box_shadow_style=\u00bbpreset4&#8243; box_shadow_horizontal=\u00bb-30px\u00bb box_shadow_vertical=\u00bb0px\u00bb box_shadow_color=\u00bbrgba(14,225,244,0.33)\u00bb global_colors_info=\u00bb{}\u00bb src__hover_enabled=\u00bbon|desktop\u00bb src__hover=\u00bbhttp:\/\/reumatologiarosario.com.ar\/web\/wp-content\/uploads\/2021\/10\/doctor-02.jpg\u00bb][\/et_pb_image][\/et_pb_column][\/et_pb_row][et_pb_row _builder_version=\u00bb4.14.1&#8243; _module_preset=\u00bbdefault\u00bb global_colors_info=\u00bb{}\u00bb][et_pb_column type=\u00bb4_4&#8243; _builder_version=\u00bb4.14.1&#8243; _module_preset=\u00bbdefault\u00bb global_colors_info=\u00bb{}\u00bb][et_pb_text _builder_version=\u00bb4.14.7&#8243; _module_preset=\u00bbdefault\u00bb global_colors_info=\u00bb{}\u00bb]<\/p>\n<p style=\"text-align: justify;\">El t\u00e9rmino LES pedi\u00e1trico se refiere al que se diagnostica en pacientes menores de 16 a\u00f1os. Este representa aproximadamente el 15-20% del total de los casos de LES. Suele iniciarse entre los 12-16 a\u00f1os, es infrecuente antes de los 10 a\u00f1os y es excepcional antes de los 5 a\u00f1os. La incidencia anual estimada es de 0.3 a 0.9 por cada 100.000 ni\u00f1os y la prevalencia, de 3.5 por cada 100.000 ni\u00f1os. Comparado con el LES del adulto el predominio femenino es menor, con una relaci\u00f3n mujeres:varones de 5:1. Los principales s\u00edntomas y signos son los mismos, pero los ni\u00f1os presentan mayor frecuencia de afectaci\u00f3n renal, neurol\u00f3gica y hematol\u00f3gica. En el adulto la relaci\u00f3n mujeres:varones es de 9:1.<\/p>\n<p style=\"text-align: justify;\"><span style=\"font-size: 14px;\">Los s\u00edntomas pueden ser variables y comunes a otras patolog\u00edas, como la presencia de fiebre, p\u00e9rdida de peso, astenia. Tambi\u00e9n puede presentarse con las denominadas alteraciones mucocut\u00e1neas:\u00a0 es decir aquellas que se presentan en mucosas y piel, como el eritema \u00aben alas de mariposa\u201d, fotosensibilidad, alopecia, fen\u00f3meno de Raynaud, livedo reticularis, exantema vascul\u00edtico, rash maculopapular, \u00falceras orales y nasales, entre otras.\u00a0<\/span><\/p>\n<p style=\"text-align: justify;\"><span style=\"font-size: 14px;\">La mayor\u00eda de los pacientes puede presentar dolores articulares y\/o musculares.<\/span><\/p>\n<p style=\"text-align: justify;\"><span style=\"font-size: 14px;\">La afectaci\u00f3n renal puede manifestarse como s\u00edndrome nefr\u00f3tico o nefr\u00edtico. Es decir que el paciente se presenta con edemas, p\u00e9rdida de prote\u00ednas por orina, alteraciones en la orina como p\u00e9rdida de cilindros y gl\u00f3bulos rojos. Tambi\u00e9n puede acompa\u00f1arse de hipertensi\u00f3n arterial y aumento en los niveles de colesterol.<\/span><\/p>\n<p style=\"text-align: justify;\"><span style=\"font-size: 14px;\">En otros casos el compromiso es hematol\u00f3gico, es decir que el paciente puede presentarse con anemia, gl\u00f3bulos blancos bajos y\/o plaquetas disminuidas.\u00a0<\/span><\/p>\n<p style=\"text-align: justify;\">En el laboratorio reumatol\u00f3gico autoinmune pueden hallarse algunas determinaciones como el FAN, o los ancticuerpos anti-ADN, aunque otras determinaciones pueden ser positivas.<\/p>\n<p style=\"text-align: justify;\">\n<p style=\"text-align: justify;\">\n<p style=\"text-align: justify;\"><strong>Referencias <\/strong><\/p>\n<ul>\n<li style=\"text-align: justify;\">Petri M, et al. Derivation and validation of the Systemic Lupus International Collaborating Clinics classification criteria for systemic lupus erythematosus. Arthritis Rheum 2012; 64:2677-86.<\/li>\n<li style=\"text-align: justify;\">Bertsias GK, et al, EULAR\/ERA-EDTA recommendations for the management of adult and paediatric lupus nephritis. Ann Rheum Dis 2012; 71:1771-82.<\/li>\n<li style=\"text-align: justify;\">Groot N, et al. European evidence-based recommendations for the diagnosis and treatment of childhood-onset lupus nephritis: the SHARE initiative. Ann Rheum Dis 2017; 76:1965-73.<\/li>\n<li style=\"text-align: justify;\">Bertsias GK, et al. EULAR recommendations for the management of systemic lupus erythematosus with neuropsychiatric manifestations: report of a task force of the EULAR standing committee for clinical affairs. Ann Rheum Dis 2010; 69:2074-82.<\/li>\n<li style=\"text-align: justify;\">Chiewchengchol D, Murphy R, Edwards SW, Beresford MW. Mucocutaneous manifestations in juvenile-onset systemic lupus erythematosus: a review of literature. Pediatr Rheumatol Online J 2015; 13:1.<\/li>\n<\/ul>\n<p>[\/et_pb_text][\/et_pb_column][\/et_pb_row][\/et_pb_section][et_pb_section fb_built=\u00bb1&#8243; admin_label=\u00bbBlog\u00bb _builder_version=\u00bb3.22&#8243; background_color=\u00bb#f1f5f7&#8243; custom_margin=\u00bb|||\u00bb custom_padding=\u00bb100px|0|100px|0px|true|false\u00bb border_radii=\u00bb||15vw||\u00bb global_colors_info=\u00bb{}\u00bb][et_pb_row _builder_version=\u00bb3.25&#8243; global_colors_info=\u00bb{}\u00bb][et_pb_column type=\u00bb4_4&#8243; _builder_version=\u00bb3.25&#8243; custom_padding=\u00bb|||\u00bb global_colors_info=\u00bb{}\u00bb custom_padding__hover=\u00bb|||\u00bb][et_pb_blog fullwidth=\u00bboff\u00bb posts_number=\u00bb6&#8243; include_categories=\u00bb4&#8243; show_author=\u00bboff\u00bb _builder_version=\u00bb4.14.1&#8243; header_level=\u00bbh4&#8243; header_font=\u00bbMontserrat||||||||\u00bb header_line_height=\u00bb1.5em\u00bb body_font=\u00bbMontserrat|300|||||||\u00bb body_font_size=\u00bb15px\u00bb body_line_height=\u00bb2em\u00bb meta_font=\u00bbMontserrat|300|||||||\u00bb pagination_font=\u00bbMontserrat||||||||\u00bb pagination_text_color=\u00bb#2f8cff\u00bb pagination_font_size=\u00bb16px\u00bb pagination_line_height=\u00bb2em\u00bb custom_padding=\u00bb||0px|||\u00bb border_radii=\u00bbon|25px|25px|25px|25px\u00bb border_width_all=\u00bb0px\u00bb box_shadow_style=\u00bbpreset3&#8243; box_shadow_vertical=\u00bb30px\u00bb box_shadow_blur=\u00bb50px\u00bb box_shadow_spread=\u00bb-30px\u00bb box_shadow_color=\u00bbrgba(0,0,0,0.1)\u00bb global_colors_info=\u00bb{}\u00bb][\/et_pb_blog][\/et_pb_column][\/et_pb_row][\/et_pb_section]<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Lupus Eritematoso Sist\u00e9mico &nbsp;El\u00a0lupus eritematoso sist\u00e9mico (LES)\u00a0es una\u00a0enfermedad autoinmune cr\u00f3nica multisist\u00e9mica\u00a0cuyas manifestaciones son muy variables.\u00a0El t\u00e9rmino LES pedi\u00e1trico se refiere al que se diagnostica en pacientes menores de 16 a\u00f1os. Este representa aproximadamente el 15-20% del total de los casos de LES. Suele iniciarse entre los 12-16 a\u00f1os, es infrecuente antes de los 10 a\u00f1os [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_et_pb_use_builder":"on","_et_pb_old_content":"","_et_gb_content_width":"","footnotes":""},"class_list":["post-501","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/reumatologiarosario.com.ar\/web\/wp-json\/wp\/v2\/pages\/501","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/reumatologiarosario.com.ar\/web\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/reumatologiarosario.com.ar\/web\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/reumatologiarosario.com.ar\/web\/wp-json\/wp\/v2\/users\/2"}],"replies":[{"embeddable":true,"href":"https:\/\/reumatologiarosario.com.ar\/web\/wp-json\/wp\/v2\/comments?post=501"}],"version-history":[{"count":8,"href":"https:\/\/reumatologiarosario.com.ar\/web\/wp-json\/wp\/v2\/pages\/501\/revisions"}],"predecessor-version":[{"id":1249,"href":"https:\/\/reumatologiarosario.com.ar\/web\/wp-json\/wp\/v2\/pages\/501\/revisions\/1249"}],"wp:attachment":[{"href":"https:\/\/reumatologiarosario.com.ar\/web\/wp-json\/wp\/v2\/media?parent=501"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}